Otogenic Sinus Thrombosis and Hemophilia: A Clinical Case

Background. Patients with hemophilia are protected from thrombosis by a deficiency of one coagulation factors, therefore thrombotic complications rare in them. Currently, few descriptions spontaneous venous adult hemophiliacs can be found the literature. Even fewer data thromboembolic reported pediatric practice. At present, no clear recommendations given for management children hemophilia, which requires further study this issue to develop prevention and treatment regimens, including otogenic sinus category patients. Case description . A 7-year-old boy was transferred Somatic Hospital Intensive Care Unit Regional Clinical No. 2 Tyumen (Russia) an Otorhinolaryngology Unit. He diagnosed non-perforative form acute right-sided suppurative otitis media, mastoiditis, right sigmoid sinus. The anamnesis shows that child is A, moderate severity (factor VIII level — 5%), he has been receiving factor replacement therapy last year. Upon admission, general blood test revealed abnormalities, slight increase acute-phase parameters: C-reactive protein, fibrinogen, signs hypocoagulation. Due negative dynamics, underwent anthromastoidotomy against background intensive therapy. Surgery presence granulation tissue hemorrhagic thrombi antrum aditus. In postoperative period, accompanied antibacterial anticoagulant Conclusion. patients hereditary difficult task. On hand, it surgical intervention order prevent thrombosis, on other hand reduce risks complications. described case demonstrates need interdisciplinary approach diagnosis patient lateral A. minimize intraoperative insure favorable outcome.